In this Issue
Editorial Message
Editorials
- Why should neurologists be interested in Williams syndrome?Michael L. Rossen, Harvey B. Sarnat
- Stiff-person syndromeStiff opposition to a simple explanationJohn T. Kissel, Rodger J. Elble
- Congenital muscular dystrophyFrom rags to richesFrancesco Muntoni, Caroline A. Sewry
In Memoriam
Articles
- Complex regional pain syndrome type I (RSD)Pathology of skeletal muscle and peripheral nerveL. van der Laan, H. J. ter Laak, A. Gabreëls-Festen, F. Gabreëls, R.J.A. Goris
- MRI evidence that docosahexaenoic acid ethyl ester improves myelination in generalized peroxisomal disordersManuela Martinez, Elida Vazquez
- Brain biochemistry in Williams syndromeEvidence for a role of the cerebellum in cognition?C. Rae, A. Karmiloff-Smith, M. A. Lee, R. M. Dixon, J. Grant, A. M. Blamire, C. H. Thompson, P. Styles, G. K. Radda
- Comparison of valproate and phenobarbital treatment after status epilepticus in ratsA. R. Bolanos, M. Sarkisian, Y. Yang, A. Hori, S. L. Helmers, M. Mikati, P. Tandon, C. E. Stafstrom, G. L. Holmes
- Vagus nerve stimulation therapy for partial-onset seizuresA randomized active-control trialA. Handforth, C. M. DeGiorgio, S. C. Schachter, B. M. Uthman, D. K. Naritoku, E. S. Tecoma, T. R. Henry, S. D. Collins, B. V. Vaughn, R. C. Gilmartin, D. R. Labar, G. L. Morris, M. C. Salinsky, I. Osorio, R. K. Ristanovic, D. M. Labiner, J. C. Jones, J. V. Murphy, G. C. Ney, J. W. Wheless
- Olfactory epileptic aurasVinita Acharya, Jayant Acharya, Hans Lüders
- Proton magnetic resonance spectroscopy in MRI-negative temporal lobe epilepsyA. Connelly, W. Van Paesschen, D. A. Porter, C. L. Johnson, J. S. Duncan, D. G. Gadian
- Relative utility of 1H spectroscopic imaging and hippocampal volumetry in the lateralization of mesial temporal lobe epilepsyR. Kuzniecky, J. W. Hugg, H. Hetherington, E. Butterworth, E. Bilir, E. Faught, F. Gilliam
- Fertility in patients with epilepsyA population-based studyElias Olafsson, Allen W. Hauser, Gunnar Gudmundsson
- Longitudinal MRI findings in pyridoxine-dependent seizuresSidney M. Gospe, Stephen T. Hecht
- Hippocampal sclerosis studied in identical twinsGraeme D. Jackson, Anne M. McIntosh, Regula S. Briellmann, Samuel F. Berkovic
- Physiologic studies of spinal inhibitory circuits in patients with stiff-person syndromeM. K. Floeter, J. Valls-Solé, C. Toro, D. Jacobowitz, M. Hallett
- Laminin α2 chain-deficient congenital muscular dystrophyVariable epitope expression in severe and mild casesR. D. Cohn, R. Herrmann, L. Sorokin, U. M. Wewer, T. Voit
- Laminin α2 muscular dystrophyGenotype/phenotype studies of 22 patientsE. Pegoraro, H. Marks, C. A. Garcia, T. Crawford, P. Mancias, A. M. Connolly, M. Fanin, F. Martinello, C. P. Trevisan, C. Angelini, A. Stella, M. Scavina, R. L. Munk, S. Servidei, C. C. Bönnemann, T. Bertorini, G. Acsadi, C. E. Thompson, D. Gagnon, G. Hoganson, V. Carver, R. A. Zimmerman, E. P. Hoffman
- Magnetic resonance imaging of muscle in amyotrophic lateral sclerosisW. W. Bryan, J. S. Reisch, G. McDonald, L. L. Herbelin, R. J. Barohn, J. L. Fleckenstein
- Decreased type IV collagen of skin and serum in patients with amyotrophic lateral sclerosisS. Ono, T. Imai, K. Takahashi, K. Jinnai, T. Yamano, K. Nagao, N. Shimizu, M. Yamauchi
- A double-blind, dose-response study of midodrine in neurogenic orthostatic hypotensionR. A. Wright, H. C. Kaufmann, R. Perera, T. L. Opfer-Gehrking, M. A. McElligott, K. N. Sheng, P. A. Low
- Regional cerebral glucose metabolism in dementia with Lewy bodies and Alzheimer's diseaseK. Ishii, T. Imamura, M. Sasaki, S. Yamaji, S. Sakamoto, H. Kitagaki, M. Hashimoto, N. Hirono, T. Shimomura, E. Mori
- Interaction of the apolipoprotein E and CI loci in predisposing to late-onset Alzheimer's diseaseEugene Drigalenko, Shirley Poduslo, Robert Elston
- Altered glucose metabolism in the hippocampal head in memory impairmentY. Ouchi, S. Nobezawa, H. Okada, E. Yoshikawa, M. Futatsubashi, M. Kaneko
- Clinicometabolic dissociation of cognitive functions and social behavior in frontal lobe lesionsM. Sarazin, B. Pillon, P. Giannakopoulos, G. Rancurel, Y. Samson, B. Dubois
- Accelerated decline in apolipoprotein E-ϵ4 homozygotes with Alzheimer's diseaseS. Craft, L. Teri, S. D. Edland, W. A. Kukull, G. Schellenberg, W. C. McCormick, J. D. Bowen, E. B. Larson
- Progression of Alzheimer's disease in black and white patientsThe CERAD experience, Part XVIG. G. Fillenbaum, B. Peterson, K. A. Welsh-Bohmer, W. A. Kukull, A. Heyman
- Cerebral infarcts in patients with autopsy-proven Alzheimer's diseaseCERAD, part XVIIIA. Heyman, G. G. Fillenbaum, K. A. Welsh-Bohmer, M. Gearing, S. S. Mirra, R. C. Mohs, B. L. Peterson, C. F. Pieper
- Stroke-attributable nursing home useA population-based studyC. L. Leibson, J. E. Ransom, R. D. Brown, W. M. O'Fallon, S. L. Hass, J. P. Whisnant
- Stroke in children and sickle-cell diseaseBaltimore-Washington Cooperative Young Stroke StudyC. J. Earley, S. J. Kittner, B. R. Feeser, J. Gardner, A. Epstein, M. A. Wozniak, R. Wityk, B. J. Stern, T. R. Price, R. F. Macko, C. Johnson, M. A. Sloan, D. Buchholz
- Relation between cerebral blood flow and neurologic deficit resolution in acute ischemic strokeAndrew D. Firlik, Giorgio Rubin, Howard Yonas, Lawrence R. Wechsler
- Angiographically defined primary angiitis of the CNSIs it really benign?A. R. Woolfenden, D. C. Tong, M. P. Marks, A. O. Ali, G. W. Albers
- Platelet activation, epinephrine, and blood pressure in obstructive sleep apnea syndromeI. Eisensehr, B. L. Ehrenberg, S. Noachtar, K. Korbett, A. Byrne, A. McAuley, T. Palabrica
- Ipsilateral motor activation in patients with cerebral gliomasM. D. Caramia, S. Telera, M. G. Palmieri, M. Wilson-Jones, A. Scalise, C. Iani, R. Giuffrè, G. Bernardi
- Dextromethorphan improves levodopa-induced dyskinesias in Parkinson's diseaseVerhagen L. Metman, Del P. Dotto, R. Natté, P. van den Munckhof, T. N. Chase
- Neuropsychological consequences of posteroventral pallidotomy for the treatment of Parkinson's diseaseLisa L. Trépanier, Jean A. Saint-Cyr, Andres M. Lozano, Anthony E. Lang
- Patients with features similar to Huntington's disease, without CAG expansion in huntingtinA. Rosenblatt, N. G. Ranen, D. C. Rubinsztein, O. C. Stine, R. L. Margolis, M. V. Wagster, M. W. Becher, A. E. Rosser, J. Leggo, J. R. Hodges, C. K. ffrench-Constant, M. Sherr, M. L. Franz, M. H. Abbott, C. A. Ross
- A phase I/II trial of nimodipine for HIV-related neurologic complicationsB. A. Navia, U. Dafni, D. Simpson, T. Tucker, E. Singer, J. C. McArthur, C. Yiannoutsos, L. Zaborski, S. A. Lipton, the AIDS Clinical Trial Group*
- Assessing information in T2-weighted MRI scans from secondary progressive MS patientsJames A. Koziol, Simone Wagner, Hans-Peter Adams
- Spinal cord atrophy and disability in MSA longitudinal studyV. L. Stevenson, S. M. Leary, N. A. Losseff, G. J. M. Parker, G. J. Barker, Y. Husmani, D. H. Miller, A. J. Thompson
- A phase II study of IV methylprednisolone in secondary-progressive multiple sclerosisD. E. Goodkin, R. P. Kinkel, B. Weinstock-Guttman, S. VanderBrug Medendorp, M. Secic, D. Gogol, J. E. Perryman, M. M. Uccelli, L. Neilley
- Idiopathic intracranial hypertension without papilledemaA case-control study in a headache centerShuu-Jiun Wang, Stephen D. Silberstein, Stephanie Patterson, William B. Young
Views & Reviews
Clinical/Scientific Notes
- The not so benign syndrome of transient headache with neurologic deficits and CSF lymphocytosisJ. Masjuan, J. Buisán, T. Frutos, C. Quereda, J. C. Álvarez-Cermeño
- Acute encephalopathy associated with vigabatrin monotherapy in patients with mild renal failureG. Ifergane, R. Masalha, R. Zigulinski, L. Merkin, I. Wirguin, Y. O. Herishanu
- Treatment of absence status in the Lennox-Gastaut syndrome with propofolD. Crouteau, M. Shevell, B. Rosenblatt, M. E. Dilenge, F. Andermann
- G20210A Prothrombin gene mutation in two siblings with cerebral venous thrombosisG. Huberfeld, N. Kubis, G. Lot, L. Ripoll, P. Chaine, L. Drouet, F. Woimant
- Spontaneous internal carotid artery dissection with isolated vagus nerve deficitMichael Moussouttas, Stanley Tuhrim
- Cerebral air embolism as a cause of stroke during cardiac catherizationChristine A.C. Wijman, Carlos S. Kase, Alice K. Jacobs, Richard E. Whitehead
- Progression of cerebral white matter hyperintensities on MRI is related to diastolic blood pressureJan H. Veldink, Philip Scheltens, Cees Jonker, Lenore J. Launer
- Facial nerve is liable to pressure palsyT. E. Poloni, I. M. Merlo, E. Alfonsi, K. Marinou-Aktipi, S. Botti, A. Arrigo, F. Taroni, M. Ceroni
- Evaluation of five primitive reflexes in 240 young adultsDevin L. Brown, Teresa L. Smith, Laurie E. Knepper
Correspondence
- Cerebral white matter lesions associated with vitamin B12 deficiencyKazumasa Sudo, Kunio Tashiro
- Cerebral white matter lesions associated with vitamin B12 deficiencyN. Stojsavljević, Z. Lević, J. Drulović
- Cybrids in Alzheimer's disease: A cellular model of the disease?Eric A. Schon, Eric A. Shoubridge, Carlos T. Moraes
- Cybrids in Alzheimer's disease: A cellular model of the disease?Russell H. Swerdlow, Davis W. Parker
- Neuronal calcium channel autoantibodies coexisting with type 1 Purkinje cell cytoplasmic autoantibodies (PCA-1 or "anti-Yo")Keiko Tanaka, Masakatsu Motomura, Yoko Nakao, Masami Tanaka, Shoji Tsuji
Corrections
Landmark Article
Landmark Article: Expedited Publication
Calendar
Newsletter
Professional Notices Section
Brief Communications
- Atypical stiff-person syndrome with spinal MRI findings, amphiphysin autoantibodies, and immunosuppressionK. Schmierer, J. M. Valdueza, A. Bender, P. DeCamilli, C. David, M. Solimena, R. Zschenderlein
- Kennedy's disease: Unusual molecular pathologic and clinical featuresP. J. Shaw, H. Thagesen, J. Tomkins, J. Y. Slade, P. Usher, A. Jackson, A. Curtis, K. Bushby, P. G. Ince
- Incidence of myasthenia gravis in the Emilia-Romagna region: A prospective multicenter studyEmilia-Romagna Study Group on Clinical and Epidemiological Problems in Neurology*
- Familial multiple symmetric lipomatosis associated with the A8344G mutation of mitochondrial DNAJ. Gámez, A. Playán, A. L. Andreu, C. Bruno, C. Navarro, C. Cervera, M. A. Arbós, S. Schwartz, J. A. Enriquez, J. Montoya
- Molecular genetic analysis of McArdle's disease in Spanish patientsA. L. Andreu, C. Bruno, J. Gamez, S. Shanske, C. Cervera, C. Navarro, M. A. Arbos, L. Tamburino, S. Schwartz, S. DiMauro
- Neuropathy in erythropoietic protoporphyriasS. A. Muley, H. A. Midani, J. M. Rank, R. Carithers, G. J. Parry
- A pilot study of L-methionine for the treatment of AIDS-associated myelopathyA. Di Rocco, M. Tagliati, F. Danisi, D. Dorfman, J. Moise, D. M. Simpson
- Neurosyphilis mimicking Miller-Fisher syndrome: A case report and MRI findingsFrank Stepper, Gerhard Schroth, Matthias Sturzenegger
- Creutzfeldt-Jakob disease with long duration and panencephalopathic lesions: Molecular analysis of one caseI. Ghorayeb, C. Series, P. Parchi, B. Sawan, S. Guez, J. L. Laplanche, S. Capellari, P. Gambetti, C. Vital
- Serotonin syndrome induced by transitioning from phenelzine to venlafaxine: Four patient reportsS. Diamond, B. J. Pepper, M. L. Diamond, F. G. Freitag, G. J. Urban, A. K. Erdemoglu
- Ipsilateral neglect during intracarotid amobarbital testD. L. Na, J. C. Adair, G. M. Kim, D. W. Seo, S. B. Hong, K. M. Heilman
- Ictal asomatognosia with hemiparesisPierre Thomas, Kimberly Giraud, Haiel Alchaar, Marcel Chatel
- Early morning dystonia in Parkinson's diseaseL. J. Currie, M. B. Harrison, J. M. Trugman, J. P. Bennett, G. F. Wooten
- Progressive dementia with parkinsonism in corticobasal and brainstem degeneration with neuronal inclusionsB. Behring, W. Beuche, H. A. Kretzschmar
- Phase 1 trial of transforming growth factor beta 2 in chronic progressive MSP. A. Calabresi, N. S. Fields, H. W. Maloni, A. Hanham, J. Carlino, J. Moore, M. C. Levin, S. Dhib-Jalbut, L. R. Tranquill, H. Austin, H. F. McFarland, M. K. Racke
- Fulminant progression of demyelinating disease after valproate-induced encephalopathyKaren A. Blindauer, Gregory Harrington, George L. Morris, Khang-Cheng Ho
- Calcific cerebral embolism in systemic calciphylaxisGeorge Katsamakis, Timothy G. Lukovits, Philip B. Gorelick
- Long-term selective IgG immunoadsorption improves Rasmussen's encephalitisC. Antozzi, T. Granata, N. Aurisano, G. Zardini, P. Confalonieri, G. Airaghi, R. Mantegazza, R. Spreafico
- Antiepileptic drug treatment following temporal lobectomyJohn Maher, Richard S. McLachlan
- A pilot study of oral sumatriptan as intermittent prophylaxis of menstruation-related migraineLawrence C. Newman, Richard B. Lipton, Christine L. Lay, Seymour Solomon
Poster Presentations: Late Breaking News
- X-linked Dominant ALSTeepu Siddique, S. Hong, B. R. Brooks, W-Y. Hung, N. A. Siddique, J. Rimmler, J. P. Kaplan, J. L. Haines, R. H. Brown, M. A. Pericak Vance
- Rett SyndromeEric P. Hoffman, N. Sirianni, J. L. Pereira, R. F. Pillotto, N. Sakkubai
- 4-Aminopyridine: Long-Term Administration to Spinal Cord Injured Humans Improves Sensorimotor Function and Is not Associated with ToxicityJack L. Segal, M. S. Pathak, P. J. Himber, J. P. Hernandez, S. R. Brunnemann, R. A. Charter
- A Two Locus Model for Hemiplegic Migraine on Chr1q and Candidate Gene ScreeningKathy Gardner, J. Badger, M. M. Barmada, J. O'Connell, E. P. Hoffman
- Pramipexole Alleviates Sensory and Motor Symptoms of Restless Legs SyndromeJacques Montplaisir, A. Nicolas, R. Denesle, B. Gomez-Mancilla
- Functional Blocking of HLA Molecules with Organic Non-Peptide Compounds Screened by Computer Modeling: Inhibition of the T Cell Response to Myelin Basic Protein (MBP)Niklas K.U. Koehler, S. Wang, M. Liu, D. Yin, X-W. Wu, J. R. Richert