RT Journal Article
SR Electronic
T1 Hereditary nonprogressive athetotic hemiplegia
JF Neurology
JO Neurology
FD Lippincott Williams & Wilkins
SP 849
OP 849
DO 10.1212/WNL.27.9.849
VO 27
IS 9
A1 FLOYD HAAR
A1 PAUL DYKEN
YR 1977
UL http://n.neurology.org/content/27/9/849.abstract
AB A family with four affected members showed a stereotyped unilateral neurologic deficit. The disorder was characterized in each member by congenital left hemiparesis, with subsequent development of left hemihypoplasia and athetoid posturing of the left hand. Although the proband was initially considered a “cerebral palsy” victim, the autosomal dominant pattern and the stereotyped clinical features in all affected family members suggest a hereditary process. Hereditary factors may be an uncommon cause of static unilateral neurologic motor defects.