Table 1.

Baseline characteristics of 367 DM patients

MenWomenTotal
* p < 0.05.
DM = myotonic dystrophy.
Age, y, n182185367
Median (range)32.0 (2–80)34.0 (4–73)33.0 (2–80)
Age at onset, y, n125130255
Median (range)17.0 (0–44*)20.0 (0–51)18.0 (0–51)
Disease duration, y, n125130255
Median (range)11.0 (0–45)13.0 (0–52)12.0 (0–52)
Affected parent, n138127265
% Mother44.243.343.8
DM phenotype, n151152303
% Congenital7.34.65.9
% Childhood11.38.69.9
% Early adult45.043.444.2
% Adult29.136.232.7
% Mild7.37.27.3
Muscular weakness, n128135263
% No weakness25.831.128.5
% Distal weakness36.736.336.5
% Proximal weakness37.532.635.0